Unilateral Pulmonary Agenesis – As a cause of respiratory distress in newborn
Abstract
Pulmonary agenesis is a rare developmental defect which occurs as a result of failure of development of primitive lung bud. The onset & mode of presentation is highly variable ranging from asymptomatic cases to cases diagnosed in adulthood due to recurrent respiratory tract infections. Around 50% of cases are associated with other congenital anomalies.Isolated U/L pulmonary agenesis, if not associated with other congenital abnormalities may have fewer symptoms & long survival. Hereby we report a case of 2 days old female baby with right lung agenesis who presented with respiratory distress in neonatal period.
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