Single coronary ostium, unilateral pulmonary atresia and MAPCA with tetralogy of fallot in a young adult: a rare association

  • Dr Keyur Vora Department of Cardiology, Care Hospitals, The Institute of Medical Sciences, Surat, Gujarat, India
Keywords: Tetralogy of Fallot, Congenital heart disease, Single coronary ostium

Abstract

Tetralogy of Fallot (TOF) is the most common form of cyanotic congenital heart disease (CHD). The mortality rate in untreated patients reaches 50% by age 6 years. It is also the most common form of cyanotic CHD with survival upto adulthood. However, TOF with both coronary and pulmonary vasculature anomalies is an extreme variant. We report a case of TOF with single coronary ostium (SCA); atretic branch pulmonary arteries and major aortopulmonary collateral artery (MAPCA) with relatively symptomless period upto 22 years of age.

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References

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Single coronary ostium, unilateral pulmonary atresia and MAPCA with tetralogy of fallot in a young adult: a rare association
CITATION
DOI: 10.17511/ijmrr.2016.i12.25
Published: 2016-12-31
How to Cite
1.
Vora K. Single coronary ostium, unilateral pulmonary atresia and MAPCA with tetralogy of fallot in a young adult: a rare association. Int J Med Res Rev [Internet]. 2016Dec.31 [cited 2021Jun.18];4(12):2226-30. Available from: https://ijmrr.medresearch.in/index.php/ijmrr/article/view/795
Section
Case Report