Neonatal Kasabach-Merritt Syndrome (KMS): case report

  • Dr. Santosh Kumar Rathia Assistant Professor, Department of paediatrics, Pt. JNM Medical College, Raipur, CG, India
  • Dr. Sharja Phuljhele Professor and Head, Department of Paediatrics, Pt. JNM Medical College, Raipur, CG, India
  • Dr. Animesh Gandhi Junior Resident, Department of Paediatrics, Pt. JNM Medical College and Dr. Bhim Rao Ambedkar Memorial Hospital, Raipur (C.G), India
Keywords: Kasabach-Merritt syndrome, Haemangioma, Thrombocytopenia, Corticosteroid, Vincristine

Abstract

A 2days baby girl presented with congenital reddish-blue swelling over chest and abdomen with thrombocytopenia. The clinical, imagining and laboratory findings suggested the diagnosis of KMS. Oral steroid was started with initially needed platelet and FFP transfusions. Large thoracic hemangioma was non-amenable to surgical and radiological interventions. Vincristine was initiated after 2week trial of Prednisolone for persistent thrombocytopenia and non-regressing haemangioma. Over a week the lesion shrunk with improving platelet count. Vincristine was stopped after 4weeks in view of no further tumour shrinkage. The patient was discharged on steroid advised for 6-12 months and showed significant tumour regression at 3month.

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Neonatal Kasabach-Merritt Syndrome (KMS): case report
CITATION
DOI: 10.17511/ijmrr.2016.i12.16
Published: 2016-12-31
How to Cite
1.
Kumar Rathia S, Phuljhele S, Gandhi A. Neonatal Kasabach-Merritt Syndrome (KMS): case report. Int J Med Res Rev [Internet]. 2016Dec.31 [cited 2021Jun.19];4(12):2176-80. Available from: https://ijmrr.medresearch.in/index.php/ijmrr/article/view/793
Section
Case Report