Cerebral astroblastoma-a rare and elusive case
Abstract
Background: Astroblastoma is rare neuroglial intracranial tumor most commonly occurring in the first three decades of life.
Case report: A 5 year old female child presented with intermittent headache, diplopia and recurrent seizures over a period of approximately 4 months. Her neurological examination revealed 6th nerve palsy and papilledema. Both CT and MRI revealed a well defined enhancing solid-cystic mass in the left fronto-parietal cerebral cortex with mass effect suggestive of primitive neuroectodermal tumor. She underwent gross total resection of the lesion through craniotomy. Histopathology along with immunohistochemistry was surprisingly suggestive of astroblastoma.
Conclusion: Astroblastomas are very rare and often misdiagnosed.
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References
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