Limb salvage in epithelioid sarcoma like hemangioendothelioma invading femur mid shaft: a case report
Keywords:
Epithelioid Sarcoma Likehemangioendothelioma, Femur, Immunohistochemistry, Limb Salvage
Abstract
Epithelioid sarcoma like hemangioendothelioma (ES-H) is recently added vascular soft tissue tumor in WHO list, with high propensity for infiltrative growth, local recurrence and low metastatic potential. We present a twenty year old male with right mid thigh swelling with pain since five months whose x-rays showed osteolytic, scalloped lesions of mid shaft femur. On workup was diagnosed ES-H for which wide excision of tumor was done and limb salvaged with biological reconstruction using free vascularised fibula.
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References
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3. Billings SD, Folpe AL, Weiss SW. Epithelioid sarcoma-like hemangioendothelioma. Am J Surg Pathol. 2003;27(1):48–57. [PubMed]
4. Watabe A, Okuyama R, Hashimoto A, Hosaka M, Hatori M, Kariya Y, et al. Epithelioid sarcoma-like haemangioendothelioma: A case report. Acta Derm Venereol. 2009;89(2):208–9. [PubMed]
5. Tokyol C, Uzüm N, Kuru I, Uluoglu O. Epithelioid sarcoma-like hemangioendothelioma. 2005;(18):436–9. [PubMed]
6. Amary MF, O’Donnell P, Berisha F, Tirabosco R, Briggs T, Pollock R, et al. Pseudomyogenic (epithelioid sarcoma-like) hemangioendothelioma: Characterization of five cases. Skeletal Radiol. 2013;42(7):947–57.
7. Miettinen M, Fanburg-Smith JC, Virolainen M, Shmookler BM, Fetsch JF. Epithelioid sarcoma: An immunohistochemical analysis of 112 classical and variant cases and a discussion of the differential diagnosis. Hum Pathol. 1999;30(8):934–42. [PubMed]
8. Requena L, Kutzner H. Hemangioendothelioma. Semin Diagn Pathol. 2013;30(1):29–44. [PubMed]
9. Friel NA, Rothenberg AC, Weiss K. Pseudomyogenic Hemangioendothelioma of Bone Initially Managed as Slipped Capital Femoral Epiphysis : A Case Report. 2014;(April):363–8.
10. McGinity M, Bartanusz V, Dengler B, Birnbaum L, Henry J. Pseudomyogenic hemangioendothelioma (epithelioid sarcomalike hemangioendothelioma, fibroma-like variant of epithelioid sarcoma) of the thoracic spine. Eur Spine J. 2013;22(SUPPL.3):506–11.

CITATION
DOI: 10.17511/ijmrr.2015.i8.168
Published: 2015-09-30
How to Cite
1.
S. Chinder P, Samorekar B, Krishnamoorthy N, B.T. R. Limb salvage in epithelioid sarcoma like hemangioendothelioma invading femur mid shaft: a case report. Int J Med Res Rev [Internet]. 2015Sep.30 [cited 2025Mar.31];3(8):906-13. Available from: https://ijmrr.medresearch.in/index.php/ijmrr/article/view/342
Section
Case Report