Mickey Mouse sign and Humming Bird sign: Diagnostic Clue of Progressive Supranuclear Palsy
Keywords:
Parkinsonism, Supranuclear palsy, Mickey Mouse sign, Retrocollis, Humming Bird sign
Abstract
Progressive supranuclear palsy is a neurodegenerative disorder. The cause of PSP is unknown. It is under diagnosed by physician and neurologist. Clinical feature of PSP resemble with parkinsonism, carticobasal degeneration, multiple system atrophy and multi infarct state. Due to common clinical feature with Parkinsonism, carticobasal degeneration, multiple system atrophy neuroimaging that can help to diagnose PSP. MRI play pivotal role in confirming the diagnosis.
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References
1. Golbe Li, Davis PH, Schoenberg BS, Duvoisin RC. Prevalence and natural history of progressive supranuclear palsy. Neurology. 1988 Jul;38(7):1031-4. [PubMed]
2. Golbe LI, Davis PH, Schoenberg BS, Duvoisin RC. Prevalence and natural history of progressive supranuclear palsy. Neurology. 1988 Jul;38(7):1031-4. [PubMed]
3. Bower JH, Maraganore DM, McDonnell SK, Rocca W.A. Incidence of progressive supranuclear palsy and multiple system atrophy in Olmsted County Minnesota, 1976 to 1990. Neurology. 1997 Nov;49(5):1284–1288. [PubMed]
4. Santacruz P, Uttl B, Litvan I, Grafman J. Progressive supranuclear palsy: a survey of disease course. Neurology. 1998 Jun;50(6):1637-47. [PubMed]
5. Ohara S, Kondo K, Morita H, maruyama K, Ikeda S, Yanagisawa N. Progressive supranuclear palsy-like syndrome in two siblings of a consanguineous marriage. Neurology. 1992 May;42(5):1009-14.
6. Davis PH, Golbe LI, Duvoisin RC, sehoenberg BS. Risk factors for progressive supranuclear palsy. Neurology. 1988 Oct;38(10):1546-52. [PubMed]
7. KR, Pearce RK Natural history of progressive supranuclear palsy (Steele-Richardson-Olszewski syndrome) and clinical predictors of survival: a clinicopathological study. J Neurol Neurosurg Psychiatry 1996; 60:615–620.
8. Daniel SE, De Bruin VMS, Lees AJ .The clinical and pathological spectrum of Steele-Richardson-Olszewski syndrome (progressive supranuclear palsy): a reappraisal. Brain 1995;118 (3):759–770. [PubMed]
9. Colosimo C, Albanese A, Hughes AJ, De bruin VMS, Lees AJ. Some specific clinical features differentiate multiple system atrophy (striatonigral variety) from Parkinson's disease. Arch Neurol 1995;52(3):294–298.
10. De Bruin VM, Lees AJ, Daniel SE. Diffuse Lewy body disease presenting with supranuclear gaze palsy, parkinsonism, and dementia: a case report. Mov Disord. 1992 Oct;7(4):355-8.
11. Amarenco P, Roullet E, Hannoun L, R Marteau. Progressive supranuclear palsy as the sole manifestation of systemic Whipple's disease treated with pefloxacine (letter). J Neurol Neurosurg Psychiatry. 1991 Dec;54(12):1121-2. [PubMed]
12. De Bruin VM, Lees AJ. Subcortical neurofibrillary degeneration presenting as Steele-Richardson-Olszewski and other related syndromes: a review of 90 pathologically verified cases. Mov Disord 1994; 9(4):381–389.
13. Troost B, Daroff R. The ocular motor defects in progressive supranuclear palsy. Ann Neurol 1977; 2(5):397–403. [PubMed]
14. Tanigawa A, Komiyama A, Hasegawa O. Truncal muscle tonus in progressive supranuclear palsy. J Neurol Neurosurg Psychiatry. 1998 Feb;64(2):190-6. [PubMed]
15. Kluin KJ, Foster NL, Berent S, Gilman S. Perceptual analysis of speech disorders in progressive supranuclear palsy. Neurology. 1993 Mar;43(3 Pt 1):563-6. [PubMed]
16. Vidailhet M, Rothwell JC, Thompson PD,AJ lees, CD Marsden.The auditory startle response in the Steele-Richardson-Olszewski syndrome and Parkinson's disease. Brain. 1992 Aug;115 ( Pt 4):1181-92. [PubMed]
17. Kato N, Arai K, Hattori T. Study of rostral midbrain atrophy in progressive supranuclear palsy. J Neurol Sci. 2003 Jun 15;210(1-2):57-60.
18. Slowinski J, Imamura A, Uitti RJ, RA Pooley, AJ Strongosky, DW Dickson, DF Broderick, ZK Wszolek. MR imaging of brainstem atrophy in progressive supranuclear palsy J Neurol. 2008 Jan;255(1):37-44.
2. Golbe LI, Davis PH, Schoenberg BS, Duvoisin RC. Prevalence and natural history of progressive supranuclear palsy. Neurology. 1988 Jul;38(7):1031-4. [PubMed]
3. Bower JH, Maraganore DM, McDonnell SK, Rocca W.A. Incidence of progressive supranuclear palsy and multiple system atrophy in Olmsted County Minnesota, 1976 to 1990. Neurology. 1997 Nov;49(5):1284–1288. [PubMed]
4. Santacruz P, Uttl B, Litvan I, Grafman J. Progressive supranuclear palsy: a survey of disease course. Neurology. 1998 Jun;50(6):1637-47. [PubMed]
5. Ohara S, Kondo K, Morita H, maruyama K, Ikeda S, Yanagisawa N. Progressive supranuclear palsy-like syndrome in two siblings of a consanguineous marriage. Neurology. 1992 May;42(5):1009-14.
6. Davis PH, Golbe LI, Duvoisin RC, sehoenberg BS. Risk factors for progressive supranuclear palsy. Neurology. 1988 Oct;38(10):1546-52. [PubMed]
7. KR, Pearce RK Natural history of progressive supranuclear palsy (Steele-Richardson-Olszewski syndrome) and clinical predictors of survival: a clinicopathological study. J Neurol Neurosurg Psychiatry 1996; 60:615–620.
8. Daniel SE, De Bruin VMS, Lees AJ .The clinical and pathological spectrum of Steele-Richardson-Olszewski syndrome (progressive supranuclear palsy): a reappraisal. Brain 1995;118 (3):759–770. [PubMed]
9. Colosimo C, Albanese A, Hughes AJ, De bruin VMS, Lees AJ. Some specific clinical features differentiate multiple system atrophy (striatonigral variety) from Parkinson's disease. Arch Neurol 1995;52(3):294–298.
10. De Bruin VM, Lees AJ, Daniel SE. Diffuse Lewy body disease presenting with supranuclear gaze palsy, parkinsonism, and dementia: a case report. Mov Disord. 1992 Oct;7(4):355-8.
11. Amarenco P, Roullet E, Hannoun L, R Marteau. Progressive supranuclear palsy as the sole manifestation of systemic Whipple's disease treated with pefloxacine (letter). J Neurol Neurosurg Psychiatry. 1991 Dec;54(12):1121-2. [PubMed]
12. De Bruin VM, Lees AJ. Subcortical neurofibrillary degeneration presenting as Steele-Richardson-Olszewski and other related syndromes: a review of 90 pathologically verified cases. Mov Disord 1994; 9(4):381–389.
13. Troost B, Daroff R. The ocular motor defects in progressive supranuclear palsy. Ann Neurol 1977; 2(5):397–403. [PubMed]
14. Tanigawa A, Komiyama A, Hasegawa O. Truncal muscle tonus in progressive supranuclear palsy. J Neurol Neurosurg Psychiatry. 1998 Feb;64(2):190-6. [PubMed]
15. Kluin KJ, Foster NL, Berent S, Gilman S. Perceptual analysis of speech disorders in progressive supranuclear palsy. Neurology. 1993 Mar;43(3 Pt 1):563-6. [PubMed]
16. Vidailhet M, Rothwell JC, Thompson PD,AJ lees, CD Marsden.The auditory startle response in the Steele-Richardson-Olszewski syndrome and Parkinson's disease. Brain. 1992 Aug;115 ( Pt 4):1181-92. [PubMed]
17. Kato N, Arai K, Hattori T. Study of rostral midbrain atrophy in progressive supranuclear palsy. J Neurol Sci. 2003 Jun 15;210(1-2):57-60.
18. Slowinski J, Imamura A, Uitti RJ, RA Pooley, AJ Strongosky, DW Dickson, DF Broderick, ZK Wszolek. MR imaging of brainstem atrophy in progressive supranuclear palsy J Neurol. 2008 Jan;255(1):37-44.
CITATION
DOI: 10.17511/ijmrr.2014.i05.16
Published: 2014-10-31
How to Cite
1.
sreeramulu D, Quraishi SS, PV H, Theja CR. Mickey Mouse sign and Humming Bird sign: Diagnostic Clue of Progressive Supranuclear Palsy. Int J Med Res Rev [Internet]. 2014Oct.31 [cited 2024Dec.23];2(5):504-6. Available from: https://ijmrr.medresearch.in/index.php/ijmrr/article/view/145
Section
Case Report